Reticular erythematous mucinosis the doctors doctor. Reticular erythematous mucinosis rem is rare form of cutaneous mucinosis. Papules small bumps develop on the midback or chest and form a netlike pattern hence the name, reticular. Dermatopatologia correlacion clinico patologica free. May be indistinguishable from localized papular mucinosis. Mucinosis eritematosa reticular actas dermosifiliograficas. The central chest andor upper back area is a preferentially involved location. The area is photosensitive and has been present for 1 year without resolution and without new lesions. Characteristic findings on physical examination reticular. Clinical features and efficacy of antimalarial treatment. Papulonodular mucinosis in systemic lupus erythematosus. Courtesy of bryan anderson, md rarely, rem may occur on the extremities, head, neck, or groin, and there has been a single report of gingival involvement in a patient with typical lesions on the chest. Although the exact etiology remains undefined, efforts to.
Pdf on dec 1, 2018, daniel morgadocarrasco and others published mucinosis cutaneas find, read and cite all the research you need. Is there a home remedy for reticular erythematous mucinosis. Cutaneous lupus mucinosis also known as papular and nodular mucinosis in lupus erythematosus, papular and nodular mucinosis of gold, and papulonodular mucinosis in lupus erythematosus is a cutaneous condition characterized by lesions that present as asymptomatic skincolored, at times reddish, 0. Centers of lesions may be slightly hyperpigmented and depressed relative to their borders generalized few to thousands of 12 mm, fleshcolored to.
Direct immunofluorescence may show linear or granular deposits of igg, igm, and c3 at the basementmembrane zone 2. Pdf reticular erythematous mucinosis syndrome with. Learn more about reticular erythematous mucinosis from related diseases, pathways, genes and ptms with the novus bioinformatics tool. Papulonodular mucinosis in systemic lupus erythematosus victoria g ortiz md a, ravi s krishnan md a, ling l chen md b, and sylvia hsu md a dermatology online journal 10 2. Jan 11, 2019 reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. Dermis sindrome rem o mucinosis reticular eritematosa. Reticular erythematous mucinosis the icd10cm alphabetical index is designed to allow medical coders to look up various medical terms and connect them with the appropriate icd codes. The reticular pattern with involvement of the midline of the chest and back, the predilection for middleaged women, the controversial relationship with. Reticular erythematous mucinosis definition of reticular. This is a 28 year old woman who presents with a reticulated rash on her chest. These conditions are associated with thyroid disease. Gaclinical presentations localized groups of 12 mm fleshcolored to erythematous papules, often in an annular arrangement, over distal extremities.
Other specified hypertrophic and atrophic conditions of skin. The reticular erythematous mucinosis syndrome is a dermal, local, diffuse, and primary type of cutaneous mucinosis mainly effecting middleaged women. Reticular erythematous mucinosis icd10cm alphabetical index. The generalised form also known as scleromyxoedema presents with widespread fleshcoloured papules arranged in lines and progressive skin thickening. Predominantly affecting middleaged women, rem syndrome skin lesions are typically located on the central area of the chest or on the upper back but may also spread to the upper abdomen. Llinear morphea with secondary mucinosisinear morphea. Reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. Other specified hypertrophic and atrophic conditions of skin short description. Initially reported as a plaquelike form of cutaneous mucinosis pcm and rem syndrome, 1 these conditions were recognized as part of the spectrum of the same disorder. Dermis mucinose eritematosa reticulada information on.
Treatment of reticular erythematous mucinosis with uva1. Papular mucinosis scleromyxedema lichen myxedematosus or papular mucinosis patients report a slow onset of asymptomatic or mildly pruritic papules, which may be localized or generalized. Background reticular erythematous mucinosis rem is an uncommon disease, the nosology and specific characteristics of which are controversial because most reports deal with single cases or small series. Reticular erythematous mucinosis rem syndrome is a rare cutaneous disease first described by steigleder et al 1 more than 30 years ago. Download dermatopatologia correlacion clinico patologica. It is described in some connective tissue diseases but never in. Reticular erythematous mucinosis rem is a rare entity characterized by infiltrated erythematous plaques on exposed areas of the thorax and back.
Mucinosis eritematosa reticular actas dermosifiliogr 2004. Dermis mucinose eritematosa reticulada information on the. Reticular erythematous mucinosis rem, rem syndrome. Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Cutaneous mucinosis is a group of conditions involving an accumulation of mucin or glycosaminoglycan in the skin and its annexes. The skin lesions usually appear on the chest and upper back.
Reticular erythematous mucinosis rem, rem syndrome, plaque. Reticular erythematous mucinosis and lupus erythematosus. What you should be alert for in the history a history of photosensitivity is commonly elicited. Mucinous disorders of the skinbeyond the dermal mucinosis. Reticular erythematous mucinosis rem is a skin condition caused by fibroblasts producing abnormally large amounts of mucopolysaccharides.
Pdf cutaneous mucinosis in mixed connective tissue disease. Llinear morphea with secondary mucinosisinear morphea with. It presents with reticular, macular lesions or erythematous papules and plaques. It has been related to sun exposure, hormonal alterations, rheumatological processes and breast cancer. There is mucin deposition in the dermis without fibroblast. Induction of the disease has been associated with viral processes, solar irradiation. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective. Grouped lesions may expand into arciform or annular plaques measuring 15 cm in diameter. On alcian blue periodic acid schiff stain, abundant mucin deposition was demonstrated in the upper reticular dermis figure 3b. It is a disease that tends to affect women in the third and fourth decades of life 187 see also. There are 0 terms under the parent term reticular erythematous mucinosis in the icd10cm alphabetical index.1486 101 191 1388 823 425 1334 155 1115 254 92 1183 971 756 607 361 60 985 404 357 561 706 716 772 618 1409 1073 1281 660 1151 1213 811 1004 32 562